Search on: PLASMA THROMBOPLASTIN COMPONENT 
Descriptors Found: 1
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Descriptor English:   Factor IX 
Descriptor Spanish:   Factor IX 
Descriptor Portuguese:   Fator IX 
Synonyms English:   Christmas Factor
Plasma Thromboplastin Component
PTC
Autoprothrombin II
Coagulation Factor IX  
Tree Number:   D12.776.124.125.375
D23.119.375
Definition English:   Storage-stable blood coagulation factor acting in the intrinsic pathway. Its activated form, IXa, forms a complex with factor VIII and calcium on platelet factor 3 to activate factor X to Xa. Deficiency of factor IX results in HEMOPHILIA B (Christmas Disease). 
Entry Combination - descr/qualif English:   Factor IX/deficiency use Hemophilia B
 
See Related English:   Coagulants
 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AN analysis
AI antagonists & inhibitors BI biosynthesis
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DU diagnostic use
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   22169 
Unique Identifier:   D005164 

Occurrence in VHL:
 

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